Procedure Guideline for Scintigraphic Imaging in Cardiac Transthyretin Amyloidosis Kardiyak Transtiretin Tip Amiloidoz Değerlendirilmesinde Sintigrafik Görüntüleme Kılavuzu


ÖZDEMİR E., COŞKUN N., Altun G. D., DEMİR H., ÖZDEMİR S., Çağlıyan F., ...More

Nuclear Medicine Seminars, vol.10, no.1, pp.90-103, 2024 (Scopus) identifier

  • Publication Type: Article / Review
  • Volume: 10 Issue: 1
  • Publication Date: 2024
  • Doi Number: 10.4274/nts.galenos.2024.0008
  • Journal Name: Nuclear Medicine Seminars
  • Journal Indexes: Scopus, Academic Search Premier
  • Page Numbers: pp.90-103
  • Keywords: Cardiac amyloidosis, scintigraphy, SPECT, SPECT/CT
  • Hatay Mustafa Kemal University Affiliated: Yes

Abstract

Amyloidosis is a systemic disorder characterized by the extracellular deposition of amyloid fibrils in various tissues, with the potential for cardiac involvement. Cardiac amyloidosis, a relatively uncommon and frequently underdiagnosed etiology of heart failure, can manifest due to the infiltration of several amyloid types into the myocardium. The definitive diagnosis typically involves an endomyocardial biopsy. Utilizing scintigraphic imaging with Technetium-99m (Tc-99m) labeled bisphosphonates can aid in the early identification of cardiac involvement and differentiate between different forms of cardiac amyloidosis. This guideline aims to support nuclear medicine practitioners in advising, performing imaging procedures, documenting findings, and interpreting results from scintigraphy involving Tc-99mlabeled bone radiopharmaceuticals for the assessment of transthyretin cardiac amyloidosis.