Neurocirugia, cilt.25, sa.3, ss.128-131, 2014 (SCI-Expanded)
A 19-year-old female with sickle cell anemia (SCD) was referred to our hospital after two daysof hospitalization at another hospital for a headache crisis. This headache crisis was due toa raised intracranial pressure; these symptoms were noted and included in her comprehen-sive list of symptoms. There was an acute drop in the hemoglobin and hematocrit levels.The cranial CT scan demonstrated a left fronto-parietal acute epidural hematoma (AEH)and a calvarial bone expansion, which was suggestive of medullary hematopoiesis. Thepatient underwent emergent craniotomy and evacuation of the hematoma. There were noabnormal findings intra-operatively apart from the AEH, except skull thickening and activepetechial bleeding from the dural arteries. Repeated CT scan showed a complete evacuationof the hematoma. The possible underlying pathophysiological mechanisms were discussed.In addition to the factors mentioned in the relevant literature, any active petechial bleedingfrom the dural arteries on the separated surface of the dura from the skull could have con-tributed to the expanding of the AEH in our patient. Neurosurgeons and other health careproviders should be aware of spontaneous AEH in patients with SCD. © 2013 Sociedad Española de Neurocirugía. Published by Elsevier España, S.L. All rights reserved.